Haematopoietic stem cell transplant for hyper-IgM syndrome due to CD40 defects: a single-centre experience
نویسندگان
چکیده
منابع مشابه
Adult allogeneic haematopoietic stem cell transplantation: a single centre experience in Malaysia.
We analysed the outcome of 104 patients from a single institution who underwent allogeneic haematopoietic stem cell transplantation (AHSCT) from their HLA-identical siblings between 1993 and 2006. Sixty-nine percent of patients had peripheral blood stem cell (PBSC) as the stem cell source and the remaining had bone marrow (BM). The majority of patients are Chinese (60%) followed by Malays (24%)...
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Australia. blaIMP-4-carrying Gram-negative organisms have led to a significant outbreak in our geographic region, but the introduction of a second MBL type is a matter of concern. The finding of a blaOXA-58-carrying A. baumannii is of interest, as this gene has only recently been reported from an ICU in Athens, Greece. This case highlights the importance of international travel in the spread of...
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Recent studies show that most patients with X-linked hyper IgM syndrome have defects in the gene for CD40 ligand. We evaluated 17 unrelated males suspected of having X-linked hyper IgM syndrome. Activated T cells from 13 of the 17 patients failed to bind a soluble CD40 construct. In these patients, the sequence of CD40 ligand demonstrated mutations. By contrast, T cells from the remaining four ...
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BACKGROUND Travel activity and travel-related risks of patients after allogeneic haematopoietic stem cell transplantation (allo-HSCT) remain largely unknown. The aim of our study was to examine travel activity after allo-HSCT including travel behaviour and travel patterns. METHODS We analysed travel characteristics of allo-HSCT recipients by using a retrospective cross-sectional survey. Allo-...
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ژورنال
عنوان ژورنال: Bone Marrow Transplantation
سال: 2018
ISSN: 0268-3369,1476-5365
DOI: 10.1038/s41409-018-0219-0